THE AIR HANDLING UNITS (AHUS) DIARIES

Close to 80% of TTP is triggered by deficient action of ADAMTS13. ADAMTS13 deficiency may be constitutive, due to biallelic ADAMTS13 pathogenic variants; or obtained, due to an inhibitory antibody. Analysis of ADAMTS13 activity is done utilizing assessments according to the potential in the protease to cleave typical VWF multimers in vitro (e.If se